A rare, inherited disease, RP causes the photoreceptor cells in the retina to progressively degenerate. This degeneration first narrows the field of vision and leads to decreased night vision. Eventually, photoreceptors deteriorate so extensively that the disease causes near blindness with only slight peripheral and a small area of central vision remaining.
The term retinitis pigmentosa (RP) refers to a set of degenerative genetic diseases that gradually kill off the light-sensing cells (rods and cones) of the retina, eventually causing blindness. It is a relatively rare genetic disorder, affecting only 1 in 4,000 people. Retinitis pigmentosa can be difficult to adapt to without proper support. Although there is currently no cure for RP, regular visits with your eye care professional are important to monitor the progression of the disease, adapt to the condition, and become aware as new RP treatments are available.
Although there are variations dictating how a person inherits and develops retinitis pigmentosa, this condition is usually characterized by the following symptoms:
Poor and narrowing peripheral (side) vision.
Difficulty seeing or driving in dimly-lit conditions. This is often called “night blindness.”
As the disease progresses, vision may narrow to just a small, central vision field or “tunnel vision.”
Difficulty discerning colors.
Problems reading or doing intricate work due to deficiencies in the central field of vision, which often disappears first.
The progression of the disease can vary significantly depending on whether the condition is inherited as a dominant or recessive trait. Regular testing is very important if you have RP for two reasons:
Eye exams and vision tests can give you an idea of how your condition is progressing so that you can be aware of and prepare for any adaptations you need to make as your vision declines.
With modern technology, there are currently efforts under way to provide treatments to slow the progression of RP, or to create solutions that simulate the behavior of healthy retina cells. We can inform you of any developments that might be able to make a positive impact in the quality of your life as you live with this condition.
If you or a loved one suffers from any of these symptoms, please contact our office today for an appointment.